- An unusual subepithelial dystrophy transmitted as an autosomal dominant
trait, also called Honeycomb Dystrophy and classified as a variant
of Reis-Bucklers'.
- Clinical features:
- Presents in childhood.
- Clinical features:
- Symptoms: may present with recurrent
painful erosions and decreased vision
- Signs
- Often difficult to differentiate Honeycomb from Reis-Bucklers
dystrophy, however in the former; the corneal surface
is smooth, corneal sensation is normal
- Typical honeycomb opacity in the corneal subepithelium
region develops in the second decade of life
- Treatment:
- Superficial corneal debridement
- Photo therapeutic keratectomy maybe required in patient with
severe recurrent erosions or reduced visual function.
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