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Oculoplastics

Cornea & External Diseases

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

Non Infectious
Cystinosis

  • Autosomal recessive metabolic disorder that causes cystine crystal deposition in multiple organs.
  • Clinical features:
    • Symptoms:
      • Glare, phophobia and mild decrease in vision as the deposits may accumulate progressively throughout the cornea and involve visual axis
      • Decreased corneal sensation
    • Signs:
      • Needle shaped, refractile, polychromatic corneal crystal deposits
      • May involve conjunctiva and iris
      • Lenticular or retinal deposits may occur in a more severe case
  • Management:
    • Treat the systemic disease.
    • Topical cysteamine drops may decrease the crystals accumulation rate.
    • Penetrating keratoplasty may be considered in severe cases.

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